Juvenile xanthogranuloma is an unusual, self-limiting dermatological disorder occurring especially in infants, late childhood and rarely in adults. It belongs to the broad group of non-Langerhans cell histiocytosis. It usually appears as solitary or multiple papules, macules or nodules several millimeters in diameter with the head and neck being the most common site of involvement and vulva being the rare site. We report two cases of juvenile xanthogranuloma in an 18 months old female and 18 months old male. The female presented with three yellow papules measuring 2-3 mm in diameter around vulva region since 4 months. Similarly, the male presented with multiple tan-orange color macules on head and forehead measuring 3-4mm in diameter since 6 months. In both the cases, a biopsy without total excision was performed. The clinical and histopathological evaluation confirmed the diagnosis of juvenile xanthogranuloma. In childhood, juvenile xanthogranuloma is necessary to differentiate from another probable differential diagnosis by biopsy.
Published in | Science Journal of Clinical Medicine (Volume 6, Issue 5) |
DOI | 10.11648/j.sjcm.20170605.14 |
Page(s) | 82-85 |
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This is an Open Access article, distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution and reproduction in any medium or format, provided the original work is properly cited. |
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Copyright © The Author(s), 2017. Published by Science Publishing Group |
Xanthogranuloma, Juvenile, Children
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APA Style
Sushmita Pradhan, Shuang Chen, Lin Xiong. (2017). Case Reports on Juvenile Xanthogranuloma and Brief Review of Literature. Science Journal of Clinical Medicine, 6(5), 82-85. https://doi.org/10.11648/j.sjcm.20170605.14
ACS Style
Sushmita Pradhan; Shuang Chen; Lin Xiong. Case Reports on Juvenile Xanthogranuloma and Brief Review of Literature. Sci. J. Clin. Med. 2017, 6(5), 82-85. doi: 10.11648/j.sjcm.20170605.14
AMA Style
Sushmita Pradhan, Shuang Chen, Lin Xiong. Case Reports on Juvenile Xanthogranuloma and Brief Review of Literature. Sci J Clin Med. 2017;6(5):82-85. doi: 10.11648/j.sjcm.20170605.14
@article{10.11648/j.sjcm.20170605.14, author = {Sushmita Pradhan and Shuang Chen and Lin Xiong}, title = {Case Reports on Juvenile Xanthogranuloma and Brief Review of Literature}, journal = {Science Journal of Clinical Medicine}, volume = {6}, number = {5}, pages = {82-85}, doi = {10.11648/j.sjcm.20170605.14}, url = {https://doi.org/10.11648/j.sjcm.20170605.14}, eprint = {https://article.sciencepublishinggroup.com/pdf/10.11648.j.sjcm.20170605.14}, abstract = {Juvenile xanthogranuloma is an unusual, self-limiting dermatological disorder occurring especially in infants, late childhood and rarely in adults. It belongs to the broad group of non-Langerhans cell histiocytosis. It usually appears as solitary or multiple papules, macules or nodules several millimeters in diameter with the head and neck being the most common site of involvement and vulva being the rare site. We report two cases of juvenile xanthogranuloma in an 18 months old female and 18 months old male. The female presented with three yellow papules measuring 2-3 mm in diameter around vulva region since 4 months. Similarly, the male presented with multiple tan-orange color macules on head and forehead measuring 3-4mm in diameter since 6 months. In both the cases, a biopsy without total excision was performed. The clinical and histopathological evaluation confirmed the diagnosis of juvenile xanthogranuloma. In childhood, juvenile xanthogranuloma is necessary to differentiate from another probable differential diagnosis by biopsy.}, year = {2017} }
TY - JOUR T1 - Case Reports on Juvenile Xanthogranuloma and Brief Review of Literature AU - Sushmita Pradhan AU - Shuang Chen AU - Lin Xiong Y1 - 2017/10/24 PY - 2017 N1 - https://doi.org/10.11648/j.sjcm.20170605.14 DO - 10.11648/j.sjcm.20170605.14 T2 - Science Journal of Clinical Medicine JF - Science Journal of Clinical Medicine JO - Science Journal of Clinical Medicine SP - 82 EP - 85 PB - Science Publishing Group SN - 2327-2732 UR - https://doi.org/10.11648/j.sjcm.20170605.14 AB - Juvenile xanthogranuloma is an unusual, self-limiting dermatological disorder occurring especially in infants, late childhood and rarely in adults. It belongs to the broad group of non-Langerhans cell histiocytosis. It usually appears as solitary or multiple papules, macules or nodules several millimeters in diameter with the head and neck being the most common site of involvement and vulva being the rare site. We report two cases of juvenile xanthogranuloma in an 18 months old female and 18 months old male. The female presented with three yellow papules measuring 2-3 mm in diameter around vulva region since 4 months. Similarly, the male presented with multiple tan-orange color macules on head and forehead measuring 3-4mm in diameter since 6 months. In both the cases, a biopsy without total excision was performed. The clinical and histopathological evaluation confirmed the diagnosis of juvenile xanthogranuloma. In childhood, juvenile xanthogranuloma is necessary to differentiate from another probable differential diagnosis by biopsy. VL - 6 IS - 5 ER -